Open AccessGeneral Anesthesia for Dental Procedures in Patients with Fibrodysplasia Ossificans Progressiva
Author(s) -
Elaine Kilmartin,
Zvi Grunwald,
Frederick S. Kaplan,
Burton L. Nussbaum
Publication year - 2014
Publication title -
anesthesia and analgesia/anesthesia and analgesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.404
H-Index - 201
eISSN - 1526-7598
pISSN - 0003-2999
DOI - 10.1213/ane.0000000000000021
Subject(s) - medicine , fibrodysplasia ossificans progressiva , anesthesia , surgery , heterotopic ossification
Fibrodysplasia ossificans progressiva (FOP) is a rare genetic condition characterized by progressive heterotopic ossification of skeletal muscle and soft connective tissues, leading to progressive ankylosis of all joints of the axial and appendicular skeleton. Cervical spine fusion, ankylosis of the temporomandibular joints, thoracic insufficiency syndrome, restrictive chest wall disease, and sensitivity to oral trauma complicate airway management and anesthesia and pose life-threatening risks.