Open AccessPyloromyotomy in a Patient with Paramyotonia Congenita
Author(s) -
Binnaz Ay,
Arzu Gerçek,
Varlk I Doğan,
Gürsu Kyan,
Ylmaz F Göğüş
Publication year - 2004
Publication title -
anesthesia and analgesia/anesthesia and analgesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.404
H-Index - 201
eISSN - 1526-7598
pISSN - 0003-2999
DOI - 10.1213/01.ane.0000093234.30458.d1
Subject(s) - medicine , remifentanil , anesthesia , sevoflurane , rocuronium , pyloromyotomy , muscle relaxant , desflurane , inguinal hernia , anesthetic , surgery , neuromuscular blockade , hernia , intubation , pylorus , propofol , stomach
A 2-mo-old infant with paramyotonia congenita was scheduled for pyloromyotomy and repair of inguinal hernia. Diagnosis of paramyotonia congenita was done with positive family history, myotonia at eyelids, provocation by cold, and electromyogram analysis. Anesthesia was induced via face mask with sevoflurane at 4 minimum alveolar anesthetic concentration in oxygen. Tracheal intubation was attempted without a neuromuscular relaxant. Anesthesia was maintained with sevoflurane at 0.5 minimum alveolar anesthetic concentration in oxygen and remifentanil infusion at a rate of 0.2 micro g. kg(-1). min(-1). After discontinuation of sevoflurane and remifentanil, the patient was awake and had full recovery of muscle activity.