Open AccessReview: Portopulmonary hypertension: challenges in diagnosis and management
Author(s) -
Patrick Troy,
Aaron B. Waxman
Publication year - 2009
Publication title -
therapeutic advances in gastroenterology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.278
H-Index - 51
eISSN - 1756-2848
pISSN - 1756-283X
DOI - 10.1177/1756283x09338431
Subject(s) - portopulmonary hypertension , medicine , liver transplantation , portal hypertension , intensive care medicine , pulmonary hypertension , clinical trial , population , transplantation , cirrhosis , environmental health
Portopulmonary hypertension is defined as the combination of pulmonary arterial hypertension with portal hypertension and presents management complications in patients awaiting liver transplantation. The combination of these vascular disorders has a marked impact on mortality. At present the recommendations for management are limited because of the paucity of definitive clinical trials. We have reviewed the available data on prevalence, diagnosis and treatment. It is clearly time to more formally approach the study of this patient population.