Open AccessUnusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
Author(s) -
Guimarães Rocha Maria Sheila,
Grangeiro Mirô Hugo Salomão,
Manfroi Gregori,
de Medeiros Dias Arthur,
Cardoso Raphaella,
Dozzi Brucki Sonia Maria
Publication year - 2021
Publication title -
case reports in neurology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.207
H-Index - 15
ISSN - 1662-680X
DOI - 10.1159/000510847
Subject(s) - single case – general neurology
Superficial siderosis (SS) of the nervous system is a rare acquired condition related to hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration. The cardinal neurological features are slowly progressive hearing loss, ataxia, and pyramidal signs. Here we describe an atypical case of infratentorial SS evolving with acute intracranial hypertension in the absence of typical chronic signs.