Open AccessPrimary Extraskeletal Osteosarcoma Arising from the Optic Nerve: A Rare Case Report
Author(s) -
Bifica Sofia Lyngdoh,
Jaya Mishra,
Biswajit Dey,
Caleb Harris,
Arindom Kakati,
Zachariah Chowdhury,
Rintu Marak,
Evarisalin Marbaniang
Publication year - 2018
Publication title -
ocular oncology and pathology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.444
H-Index - 10
eISSN - 2296-4681
pISSN - 2296-4657
DOI - 10.1159/000486420
Subject(s) - medicine , ethmoidectomy , optic nerve , radiation therapy , lesion , osteosarcoma , osteotomy , diplopia , radiology , surgery , anatomy , pathology , maxillary sinus
Orbital location of extraskeletal osteosarcoma is extremely rare with only 4 cases reported so far in the English literature. We present the case of a 32-year-old female who presented with proptosis and complete loss of vision of the left eye. Contrast-enhanced computed tomography scan showed a densely calcified lobulated lesion in the left optic nerve showing strong enhancement. A left fronto-occipito-zygomatic osteotomy was conducted and a greyish brown tumor was identified. Histopathological and immunohistochemical examination of the curetted material revealed it to be extraskeletal osteosarcoma. A left partial maxillectomy with ethmoidectomy and left orbital exenteration was done and the patient was advised chemotherapy with radiotherapy.