Open AccessAggressive Angiomyolipomas: the Clandestine Epithelioid Variant
Author(s) -
Anton Maré,
Shehan Wickramasinghe,
Victor Ilie,
Maurice Mulcahy
Publication year - 2016
Publication title -
current urology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.476
H-Index - 13
eISSN - 1661-7657
pISSN - 1661-7649
DOI - 10.1159/000442853
Subject(s) - angiomyolipoma , medicine , epithelioid cell , pathology , metastasis , kidney , cancer , immunohistochemistry
Epithelioid angiomyolipoma is a rare mesenchymal derived neoplasm of the kidney. Thought to be a variant of classical angiomyolipoma, a benign tumour, its malignant potential has been highlighted by case reports of loco-regional and distant metastasis. Given the potentially adverse clinical course associated with epithelioid angiomyolipoma compared to classical angiomyolipoma, the distinction and comprehensive histological characterisation of this rare entity is essential.