Open AccessCT-Scans of Cochlear Implant Patients with Characteristics of Pendred Syndrome
Author(s) -
Sebastian Roesch,
Gerhard Moser,
Gerhard Rasp,
Miklós Tóth
Publication year - 2013
Publication title -
cellular physiology and biochemistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.486
H-Index - 87
eISSN - 1421-9778
pISSN - 1015-8987
DOI - 10.1159/000356636
Subject(s) - vestibular aqueduct , medicine , cochlear implant , temporal bone , magnetic resonance imaging , sensorineural hearing loss , cochlea , radiology , audiology , hearing loss , anatomy
Sensorineural hearing loss (SNHL) in newborns is estimated with an incidence around 1:10,000 per year and is divided into syndromic and non-syndromic forms. In case of present retrocochlear function' cochlear implantation allows speech and cognitive development in affected children, comparable to that of normal hearing children. Pathogenesis of SNHL remains unclear in many cases. Imaging of the temporal bone, such as computed tomography (CT) and magnetic resonance imaging (MRI), can reveal conspicuous findings, e.g. enlarged vestibular aqueduct (EVA) and Mondini malformation (MM) of the cochlea. These malformations can be a clinical sign for Pendred syndrome.