Open AccessExtraskeletal myxoid chondrosarcoma: a case report of complete remission by chemotherapy and review of the literature
Author(s) -
Ke Han,
Yaping Sun,
Zhihua Shen,
Jianjun Zhang,
Feng Lin,
Hui Zhao,
Saleem Meerani,
Yang Yao
Publication year - 2010
Publication title -
bmj case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.231
H-Index - 26
ISSN - 1757-790X
DOI - 10.1136/bcr.07.2009.2128
Subject(s) - medicine , chondrosarcoma , chemotherapy , soft tissue , sarcoma , rare disease , radiology , complete remission , surgery , pathology , disease
Extraskeletal myxoid chondrosarcoma is a rare soft tissue sarcoma. Surgery is the cornerstone of the management of this tumour. The response rate to chemotherapy has been very poor; with the exception of one reported case which showed promising results, overall results are disappointing because no significant radiologic or clinical responses have been noted with chemotherapy. Here we report the case of a 15-year-old girl who presented with extraskeletal myxoid chondrosarcoma in the sacrococcygeal region which was regarded as unresectable. After four cycles of chemotherapy the mass showed complete remission which has lasted >6 months.