Open AccessUnusual variant of pseudo prune belly syndrome
Author(s) -
Arun Loganathan,
Ravi Kishore Barla S S,
Jujju Jacob Kurian
Publication year - 2020
Publication title -
bmj case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.231
H-Index - 26
ISSN - 1757-790X
DOI - 10.1136/bcr-2020-236611
Subject(s) - prune belly syndrome , medicine , ureterostomy , nephrectomy , abdominal wall , surgery , vesicoureteric reflux , rare disease , reflux , disease , kidney , bladder cancer , cancer , cystectomy
Unilateral pseudo prune belly syndrome (PPBS) is a rare variant with only two other cases found in the main literature until. We present a 9-month old boy with left-sided lax abdominal wall, undescended testes and major vesicoureteric reflux involving only the left side. He underwent left orchidopexy and left end ureterostomy followed by left nephrectomy. Unilateral variant supports the theory of mesodermal arrest as a cause for prune belly syndrome. Treatment is individualised and prognosis is relatively better when compared with other variants of PPBS.