Open AccessAcute haemorrhagic oedema of infancy: a condition that is not always benign
Author(s) -
U Cucinotta,
Francesca Mazza,
Giovanni Battista Pajno,
Romina Gallizzi
Publication year - 2020
Publication title -
bmj case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.231
H-Index - 26
ISSN - 1757-790X
DOI - 10.1136/bcr-2020-236059
Subject(s) - medicine , presentation (obstetrics) , limiting , pediatrics , purpura (gastropod) , dermatology , differential diagnosis , rare disease , surgery , disease , pathology , mechanical engineering , ecology , engineering , biology
Acute haemorrhagic oedema of infancy (AHOI) is a rare condition and an unusual diagnosis for the paediatrician, as approximately 300 cases have been reported in literature so far. Although it was considered for years a less serious variant of Henoch-Schönlein purpura, nowadays it is thought to be a different entity, with his own characteristics and clinical outcome. In literature it is described as a benign condition, self-limiting and without any systemic involvement in most of the cases. We present an atypical case of AHOI with a severe presentation and which needed an aggressive and prolonged steroid therapy.