Open AccessIntractable chronic otitis media, rhinosinusitis and facial palsy: a case of active granulomatosis with polyangiitis
Author(s) -
Kwee Yen Goh,
Ross Ban,
Helin Nie Darat,
Bhaskar Ram,
Raghav C. Dwivedi
Publication year - 2020
Publication title -
bmj case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.231
H-Index - 26
ISSN - 1757-790X
DOI - 10.1136/bcr-2019-233685
Subject(s) - medicine , granulomatosis with polyangiitis , otitis , etiology , dermatology , rare disease , vasculitis , facial paralysis , disease , surgery , pathology
Granulomatosis with polyangiitis (GPA) is a rare systemic disease of unknown aetiology, characterised by necrotising granuloma formation and diffuse vasculitis. It typically affects the upper and lower respiratory tract in addition to the kidneys. Without treatment, the 2-year mortality rate exceeds 90%. We describe a presentation of intractable serous otitis media, rhinosinusitis, fever and unilateral facial palsy in an 18-year-old man with learning difficulties, which highlights the need for a high index of suspicion in diagnosing and treating this enigmatic disease.