Open AccessPrimary Ewing’s sarcoma of the temporal bone: a rare entity and review of the literature
Author(s) -
Jeewan Ram Vishnoi,
Vijay Kumar,
Kirti Srivastava,
Sanjeev Misra
Publication year - 2019
Publication title -
bmj case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.231
H-Index - 26
ISSN - 1757-790X
DOI - 10.1136/bcr-2019-230768
Subject(s) - medicine , sarcoma , pelvis , primary bone , radiation therapy , ewing's sarcoma , radiological weapon , rare disease , radiology , chemotherapy , pathology , surgery , disease
Ewing's sarcoma (ES) is the second most common malignant primary bone tumour in children and adolescents. It primarily affects the diaphysis of long bones and pelvis. ES arising from temporal bone is extremely rare. To date, 43 such cases have been described in the literature. Clinical and radiological features are non-specific. Diagnosis is based mainly on immunohistochemistry. The present article presents an extremely rare case of ES of the temporal bone in a 20-year young man, and he was successfully treated with multiagent chemotherapy and radiotherapy.