Open AccessRare neonatal interstitial lung disease masquerading as pulmonary hemosiderosis
Author(s) -
Viraraghavan Vadakkencherry Ramaswamy,
Sushma Nangia,
Anu Thukral,
Varinder Singh
Publication year - 2019
Publication title -
bmj case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.231
H-Index - 26
ISSN - 1757-790X
DOI - 10.1136/bcr-2018-228398
Subject(s) - medicine , hemosiderosis , respiratory distress , interstitial lung disease , lung biopsy , bronchoscopy , lung , pulmonary hypertension , respiratory disease , intensive care medicine , pediatrics , surgery
A preterm 32-week neonate presented on the 14th day of life with respiratory distress and cyanosis. The respiratory distress worsened progressively, which was managed with continuous positive airway pressure support. The neonate had blood-tinged oral secretions on the 39th day of life, for which bronchoscopy was performed, whose findings were suggestive of pulmonary hemosiderosis. Lung biopsy confirmed the diagnosis of pulmonary interstitial glycogenosis with pulmonary arterial hypertension. The neonate was treated successfully with systemic corticosteroids and discharged home at 3 months of age.