Open AccessAtypical presentation of IgG4 sclerosing cholangitis
Author(s) -
Harrison Roocroft,
Prashantha Sambaiah,
Ahmed Monier
Publication year - 2019
Publication title -
bmj case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.231
H-Index - 26
ISSN - 1757-790X
DOI - 10.1136/bcr-2018-228374
Subject(s) - medicine , autoimmune pancreatitis , magnetic resonance cholangiopancreatography , presentation (obstetrics) , magnetic resonance imaging , abdominal pain , pancreatitis , obstructive jaundice , rare disease , gastroenterology , jaundice , acute pancreatitis , endoscopic retrograde cholangiopancreatography , primary sclerosing cholangitis , disease , radiology
IgG 4 sclerosing cholangitis (ISC) is a rare disease which usually presents in patients in their 60's or above. Patients often present with obstructive jaundice as the first symptom, especially when associated with autoimmune pancreatitis. We report the case of a 20-year-old man who presented with acute abdominal pain, which was subsequently diagnosed as ISC in addition to autoimmune pancreatitis following magnetic resonance cholangiopancreatography (MRCP). The patient was thus treated with steroids.