Successful liver transplantation in common variable immune deficiency with reversal of hepatopulmonary syndrome | Zendy

Ross Apostolov | Zendy; Marie Sinclair | Zendy; Julie Lokan | Zendy; Peter Angus | Zendy

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Successful liver transplantation in common variable immune deficiency with reversal of hepatopulmonary syndrome

Author(s) -

Ross Apostolov,

Marie Sinclair,

Julie Lokan,

Peter Angus

Publication year - 2019

Publication title -

bmj case reports

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.231

H-Index - 26

ISSN - 1757-790X

DOI - 10.1136/bcr-2018-226095

Subject(s) - common variable immunodeficiency , hepatopulmonary syndrome , liver transplantation , medicine , liver disease , complication , liver function tests , liver function , transplantation , gastroenterology , immunology , antibody

Common variable immune deficiency (CVID) is a primary immunodeficiency disorder that is associated with abnormal liver function tests, however advanced liver disease is uncommon. Hepatopulmonary syndrome (HPS) is a rare but debilitating complication of CVID-associated liver disease. We report a case of CVID complicated by HPS that was successfully treated with orthotopic liver transplant, with the patient recovering to normal hepatic function and successfully weaning off domiciliary oxygen post-transplantation.

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