Open AccessChronic thromboembolic pulmonary hypertension: an enigma
Author(s) -
Suraj Kumar Kulkarni,
Shivakumar Bhairappa,
Amardeep Bishnoi,
Prakash Sadashivappa Surhonne
Publication year - 2018
Publication title -
bmj case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.231
H-Index - 26
ISSN - 1757-790X
DOI - 10.1136/bcr-2018-225764
Subject(s) - medicine , chronic thromboembolic pulmonary hypertension , pulmonary thromboendarterectomy , thrombus , pulmonary hypertension , cardiology , pulmonary vasculature , pulmonary embolism , work up , radiology
Chronic thromboembolic pulmonary hypertension (CTEPH) is a form of pulmonary arterial hypertension (PAH) in which the pulmonary thrombus fails to resolve, resulting in occlusion and remodelling of pulmonary arteries. 1 Timely diagnosis is critical since it is potentially curable by pulmonary thromboendarterectomy. Twenty five per cent of cases do not have a history of thromboembolic event. The diagnosis should be considered in the diagnostic work-up of PAH despite lack of history of episodes of thromboembolism. Here we are reporting a case of CTEPH with multiple systemic to pulmonary collaterals delineated by angiogram and CT.