Reversal of cardiomyopathy in propionic acidemia after liver transplantation: a 10‐year follow‐up
Author(s) -
Arrizza Chiara,
De Gottardi Andrea,
Foglia Ezio,
Baumgartner Matthias,
Gautschi Matthias,
Nuoffer JeanMarc
Publication year - 2015
Publication title -
transplant international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.998
H-Index - 82
eISSN - 1432-2277
pISSN - 0934-0874
DOI - 10.1111/tri.12677
Subject(s) - medicine , propionic acidemia , cardiomyopathy , liver transplantation , transplantation , complication , heart transplantation , cardiology , heart failure
Summary Cardiomyopathy is a frequent complication in propionic acidemia. It is mostly rapidly fatal and independent of the metabolic control or medical intervention. Here, we present the reversal of a severe cardiomyopathy after liver transplantation in a patient with propionic acidemia and the long‐term stability after ten years. Liver transplantation in patients with propionic acidemia may be considered a valid and long‐lasting treatment when cardiomyopathy is progressive and unresponsive to medical therapy.
Accelerating Research
Robert Robinson Avenue,
Oxford Science Park, Oxford
OX4 4GP, United Kingdom
Address
John Eccles HouseRobert Robinson Avenue,
Oxford Science Park, Oxford
OX4 4GP, United Kingdom