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Pleuroparenchymal fibroelastosis in association with carcinomas
Author(s) -
Baroke Eva,
Heussel Claus Peter,
Warth Arne,
Eichinger Monika,
Oltmanns Ute,
Palmowski Karin,
Herth Felix J.F.,
Kreuter Michael
Publication year - 2016
Publication title -
respirology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.857
H-Index - 85
eISSN - 1440-1843
pISSN - 1323-7799
DOI - 10.1111/resp.12654
Subject(s) - medicine , etiology , malignancy , pathology , idiopathic pulmonary fibrosis , fibrosis , disease , dermatology , lung
PPFE is a rare disease characterized by upper lobe pleural fibrosis and parenchymal fibroelastosis. Its aetiology is considered idiopathic, although possible causative factors have been described. An association of PPFE with solid tumours is unknown and has not been considered previously. We identified six patients with PPFE , four of them with a coexisting malignancy. The case series suggests that PPFE might be an implication of varying factors rather than being an exclusively idiopathic condition.