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Pediatric split liver transplantation after F ontan procedure in left isomerism combined with biliary atresia: A case report
Author(s) -
Youn Joong Kee,
Lee JeongMoo,
Yi NamJoon,
Choi Young Rok,
Suh SukWon,
You Tae,
Lee KwangWoong,
Jung ChulWoo,
Lee Jiwon,
Bae EunJung,
Ko Jae Sung,
Kim WoongHan,
Park KwiWon,
Suh KyungSuk
Publication year - 2014
Publication title -
pediatric transplantation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.457
H-Index - 69
eISSN - 1399-3046
pISSN - 1397-3142
DOI - 10.1111/petr.12364
Subject(s) - medicine , biliary atresia , liver transplantation , heterotaxy , ventricle , fontan procedure , transplantation , surgery , hypoplastic left heart syndrome , heart transplantation , pulmonary atresia , heart disease , cardiology
LI is a subset of the heterotaxy syndrome and a rare birth defect that involves the heart and other organs. It can be combined with extracardiac abnormalities, especially BA . CHD can be associated with LI in up to 15% of cases, although it is rare in BA . Pediatric LT for a child with ESLD due to BA combined with LI and CHD is a challenging issue for a transplant surgeon. Herein, we report a successful split LT on a three‐yr‐old boy with LI who survived after a Fontan procedure due to single ventricle, but who suffered from HPS associated with BA .