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Orthotopic heart transplantation in two infants with histiocytoid cardiomyopathy and left ventricular non‐compaction
Author(s) -
Siehr Stephanie L.,
Bernstein Daniel,
Yeh Justin,
Berry Gerald J.,
Rosenthal David N.,
Hollander Seth A.
Publication year - 2013
Publication title -
pediatric transplantation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.457
H-Index - 69
eISSN - 1399-3046
pISSN - 1397-3142
DOI - 10.1111/petr.12141
Subject(s) - medicine , heart transplantation , cardiology , cardiogenic shock , heart failure , cardiomyopathy , transplantation , ventricular assist device , myocardial infarction
HC is a rare cause of congestive heart failure that typically presents with malignant ventricular arrhythmias in infants, often requiring urgent intervention. Successful heart transplantation in a patient with HC has only been reported once (J Heart Lung Transplant 2004: 23: 902). The combination of HC with concurrent LVNC has only been described three times (Int J Legal Med 2009: 123: 47; Hum Pathol 2005: 36: 403; Pediatr Dev Pathol 2012: 15: 397). We report two rare cases of HC with LVNC in two infants presenting with cardiogenic shock, one requiring ECMO support who was successfully bridged to orthotopic heart transplantation with a Berlin Heart LVAD.