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Displacement of the anterior leaflet of the tricuspid valve: Rare variant of Ebstein's anomaly
Author(s) -
Tsujii Nobuyuki,
Kurosaki Kenichi,
Yasuda Kenji,
Mizuno Masanori,
Sakaguchi Heima,
Hoashi Takaya,
Ichikawa Hajime,
Shiraishi Isao
Publication year - 2016
Publication title -
pediatrics international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.49
H-Index - 63
eISSN - 1442-200X
pISSN - 1328-8067
DOI - 10.1111/ped.12962
Subject(s) - medicine , tricuspid valve , ventricle , ebstein's anomaly , anatomy , ebstein anomaly , displacement (psychology) , leaflet (botany) , cardiology , psychology , paleontology , psychotherapist , biology
In Ebstein's anomaly, the points of attachment, or hinges, of the septal and mural leaflets in the right ventricle are displaced away from the atrioventricular junction. In contrast, the junctional hinge of the anterior leaflet usually retains a normal position. Here, we report a case of giant right atrial aneurysm due to isolated displacement of the anterior leaflet of the tricuspid valve in an infant, a rare variant of Ebstein's anomaly. Enlargement of the right atrium, which was initially diagnosed during the fetal period, progressively and markedly dilated after birth and was successfully treated with surgical resection. Isolated displacement of the anterior leaflet should be recognized as a variant of Ebstein's anomaly.