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Functional total anomalous pulmonary venous connection via levoatriocardinal vein
Author(s) -
Hayashi Taiyu,
Ozawa Katsusuke,
Sugibayashi Rika,
Wada Seiji,
Ono Hiroshi
Publication year - 2016
Publication title -
pediatrics international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.49
H-Index - 63
eISSN - 1442-200X
pISSN - 1328-8067
DOI - 10.1111/ped.12920
Subject(s) - medicine , total anomalous pulmonary venous connection , cardiology , ventricle , superior vena cava , double outlet right ventricle , pulmonary vein , left atrium , venous blood , vein , lower limbs venous ultrasonography , left pulmonary vein , ablation , atrial fibrillation
We report a fetal case of double outlet right ventricle, mitral atresia, and intact atrial septum. Although the pulmonary veins were connected to the left atrium, pulmonary venous blood drained into the right superior vena cava via the stenotic levoatriocardinal vein (LACV), which resulted in a circulation resembling total anomalous pulmonary venous connection (TAPVC) with pulmonary venous obstruction. Since the pulmonary veins were connected to both the stenotic LACV and the “dead‐end” left atrium, the pulmonary venous flow had a to‐and‐fro pattern along with atrial relaxation and contraction. Postnatal echocardiography and computed tomography confirmed the diagnosis of normally connected but anomalously draining pulmonary veins via the LACV. Surgical creation of an atrial septal defect on the day of birth successfully relieved pulmonary venous obstruction. Normally connected but anomalously draining pulmonary veins via the LACV should be considered for TAPVC differential diagnosis in fetuses with a left‐side heart obstruction.