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Rectal duplications accompanying rectovestibular fistula: Report of two cases
Author(s) -
Pampal Arzu,
Ozbayoglu Asli,
Kaya Cem,
Pehlivan Yildiz,
Poyraz Aylar,
Ozen I. Onur,
Percin Ferda E.,
Demirogullari Billur
Publication year - 2013
Publication title -
pediatrics international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.49
H-Index - 63
eISSN - 1442-200X
pISSN - 1328-8067
DOI - 10.1111/ped.12086
Subject(s) - medicine , perineum , fistula , anorectal anomalies , anatomy , anus , surgery
Rectal duplication ( RD ) cysts are rare congenital anomalies that can be diagnosed with the presence of another opening in the perineum. They seldom accompany anorectal malformations ( ARM ). Two cases of RD accompanying ARM at opposite ends of the phenotypic spectrum, are described. A 3‐month‐old baby and a 2‐year‐old girl with ARM were scheduled for posterior sagittal anorectoplasty. The infant had an orifice at the anal dimple and the other had an orifice at the vestibulum posterior to the rectovestibular fistula. The infant presented with no other anomalies whereas the older one presented with an unusual coexistence of caudal duplication and caudal regression syndromes. Perioperatively both orifices were found to be related to retrorectal cysts, and were excised. Clinicians should always be alert when dealing with complex malformations. Because these malformations have variable anatomical and clinical presentations, they can represent a diagnostic and therapeutic challenge.