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Episodic idiopathic systemic capillary leak syndrome in a girl
Author(s) -
Milani Gregorio Paolo,
Dellepiane Rosa Maria,
Castellazzi Massimo Luca,
Mazzoni Marta Benedetta Maria,
Bianchetti Mario Giovanni,
Fossali Emilio Filippo
Publication year - 2013
Publication title -
pediatrics international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.49
H-Index - 63
eISSN - 1442-200X
pISSN - 1328-8067
DOI - 10.1111/ped.12068
Subject(s) - medicine , methylprednisolone , leak , circulatory system , shock (circulatory) , circulatory collapse , circulatory failure , anesthesia , cardiology , environmental engineering , engineering
Episodic idiopathic systemic capillary leak syndrome is a rare disorder that presents with attacks of circulatory shock due to plasma leakage into the extravascular space. Reported here is the case of a girl who had recurrent circulatory shock. The diagnosis of episodic idiopathic systemic capillary leak syndrome was made following the fourth episode. The course was favorable following acute i.v. cristalloids and methylprednisolone.