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Kaposiform hemangioendothelioma with overlapping features of rapidly involuting congenital hemangioma and a delayed complication of necrotizing fasciitis
Author(s) -
Belmesk Lina,
Dubois Josée,
CaouetteLaberge Louise,
David Michèle,
Bortoluzzi Patricia,
Kokta Victor,
Hatami Afshin,
McCuaig Catherine C.
Publication year - 2020
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.14262
Subject(s) - medicine , fasciitis , hemangioendothelioma , hemangioma , surgery , forearm , lymphangiomatosis , complication , kasabach–merritt syndrome , dermatology , pathology , lymphatic system
We report the case of a male infant born at term with kaposiform hemangioendothelioma (KHE) of the right forearm and coagulopathy. Our case was unusual as it involuted leaving subcutaneous atrophy and prominent veins, which are more commonly observed in rapidly involuting congenital hemangioma. At 3 years of age, the child developed recurrent superficial thrombophlebitis localized to the area where the KHE had regressed. Subsequently, he developed necrotizing fasciitis and thrombotic veins in the same location and group A streptococcal septic shock.