Premium
A case of multiple cerebral cavernomas associated with en coup de sabre scleroderma
Author(s) -
Alwash Noor,
Dinani Naila,
Felton Jessie
Publication year - 2019
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.14052
Subject(s) - medicine , scleroderma (fungus) , forehead , scalp , localized scleroderma , dermatology , neuroimaging , pathology , surgery , lichen sclerosus , psychiatry , inoculation
Linear scleroderma is a form of localized scleroderma that presents as band‐like sclerotic lesions. When it occurs on the scalp or forehead, it is called “en coup de sabre scleroderma" (ECDS). Extracutaneous associations, mostly neurologic, have been described with ECDS. We report a patient with ECDS associated with multiple cerebral cavernomas. This serves to highlight the importance of neuroimaging and multidisciplinary team involvement in patients with ECDS.