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Multifocal lymphangioendotheliomatosis without thrombocytopenia or clinical signs of systemic bleeding
Author(s) -
Peña Merino Lander,
López Almaraz Ricardo,
Fernández de Larrinoa Aitor,
Rubio Lombraña Marta,
GonzálezHermosa Maria Rosario
Publication year - 2019
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.13959
Subject(s) - medicine , gastrointestinal bleeding , disease , vascular disease , dermatology , surgery
Multifocal lymphangioendotheliomatosis with thrombocytopenia (MLT) is an extremely rare recently described disorder characterized by diffuse congenital skin and gastrointestinal vascular lesions that may be associated with gastrointestinal bleeding and thrombocytopenia. We herein present a case report of multifocal lymphangioendotheliomatosis without thrombocytopenia or extensive extracutaneous involvement (gastrointestinal bleeding). Given the high morbidity and mortality associated with this disease, it is important for clinicians to recognize this disorder in order to select the most appropriate therapeutic approach.