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In utero development of epidermolysis bullosa acquisita
Author(s) -
Dewan Anna K.,
Braue Jonathan,
Danford Brandon,
Stack Lawrence B.,
Boyd Alan S.,
Fine JoDavid,
Albers Sharon E.
Publication year - 2018
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.13704
Subject(s) - epidermolysis bullosa acquisita , medicine , epidermolysis bullosa , in utero , dermatology , pregnancy , fetus , immunology , genetics , biology , antibody , bullous pemphigoid
Abstract We report the case of an infant born with perioral vesicles that rapidly spread to involve his mouth and the majority of his body. Histopathology, immunofluorescence, and enzyme‐linked immunohistochemistry assays confirmed a diagnosis of epidermolysis bullosa acquisita ( EBA ). His mother had no history of EBA , and serum indirect immunofluorescence was negative. The patient improved rapidly with local wound care and oral dapsone.