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Management of a rare presentation of Kindler disease with digital constriction bands—Case report
Author(s) -
Ting Jeannette W. C.,
Kaur Sarbjit,
Ogboli Malobi,
Irani Kiri,
Jester Andrea
Publication year - 2018
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.13674
Subject(s) - medicine , dermatology , epidermolysis bullosa , presentation (obstetrics) , poikiloderma , disease , atrophy , constriction , surgery , pathology
Kindler disease is a type of epidermolysis bullosa associated with acral blistering, diffuse cutaneous atrophy, poikiloderma, mucosal stenosis, and photosensitivity. This is the first case report in the literature to describe constriction bands associated with Kindler disease causing ischemia of the fingertips requiring urgent release and full‐thickness skin grafts. Dermatologists reviewing such patients need to be aware of this condition and refer to a children's hand surgeon early to avoid leaving patients with prolonged periods of pain.