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Pediatric Pemphigus Herpetiformis: Case Report and Review of the Literature
Author(s) -
Peterman Caitlin M.,
Vadeboncoeur Sophie,
Schmidt Birgitta A.,
Gellis Stephen E.
Publication year - 2017
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.13152
Subject(s) - medicine , dapsone , dermatology , dermatitis herpetiformis , prednisone , rash , pemphigus , pemphigus vulgaris , first line therapy , pediatrics , pathology , surgery , disease
Pemphigus herpetiformis ( PH ) is a rare autoimmune bullous condition usually seen in adults and likely underrecognized in children. We describe a 2‐year‐old girl who presented with a chronic, generalized, blistering rash consistent with pediatric PH based on histology and immunohistochemistry and review the literature. Prognosis is generally more favorable in children than adults. Prednisone and dapsone should be considered as first‐line agents to induce remission.