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Kaposiform Hemangioendothelioma Presenting as Hydrops Fetalis
Author(s) -
SobrinoFernández Elena,
CamposDomínguez Minia,
GregorioHernández Rebeca,
HuertaAragonés Jorge,
BeléndezBieler Cristina,
LancharroZapata Ángel,
FrancoFernández María Luisa,
BernardoAtienza Belén,
SánchezLuna Manuel
Publication year - 2017
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.13101
Subject(s) - medicine , hydrops fetalis , vincristine , prednisone , hemangioendothelioma , angiosarcoma , surgery , cyclophosphamide , pathology , fetus , chemotherapy , pregnancy , genetics , biology
We describe the case of a 33‐week preterm infant who developed nonimmune hydrops fetalis secondary to a kaposiform hemangioendothelioma ( KHE ). The tumor was successfully treated with vincristine, prednisone, ticlopidine, and aspirin. KHE can be an unusual cause of hydrops fetalis; in such cases, diagnosis can be challenging since generalized edema can obscure KHE .