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Harlequin Ichthyosis: A Surgical Perspective
Author(s) -
Pet Mitchell A.,
Gupta Deepti,
Tse Raymond W.
Publication year - 2016
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.12944
Subject(s) - medicine , ichthyosis , intervention (counseling) , perioperative , amputation , surgery , surgical procedures , perspective (graphical) , dermatology , nursing , artificial intelligence , computer science
Limb constriction or encasement in patients with harlequin ichthyosis can cause tissue injury resulting in necrosis and auto‐amputation. Surgical release of constrictive plaques has been previously demonstrated, but the perioperative and intraoperative considerations surrounding this infrequent intervention have not been discussed in detail. This report documents a case of harlequin ichthyosis requiring surgical treatment, focusing on the importance of early surgical consultation, risks of surgery, indications for and timing of surgical intervention, and the details of the operation.