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Bullous Kaposiform Hemangioendothelioma Masquerading as Aplasia Cutis Congenita
Author(s) -
Steen Aaron J.,
Shin Joseph H.,
Pace Nicole C.,
Edgar Mark,
Clay Michael R.,
Linos Konstantinos,
Barton Dorothea T.,
Mann Julianne A.
Publication year - 2016
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.12890
Subject(s) - medicine , consumptive coagulopathy , aplasia cutis congenita , scalp , dermatology , coagulopathy , hemangioendothelioma , pathology , surgery
We present the case of a male infant with violaceous bullae on the scalp that were initially thought to be bullous aplasia cutis but at 3 months of age were diagnosed as a kaposiform hemangioendothelioma. This diagnosis should be considered when evaluating newborns with bullous plaques on the scalp that do not heal in the first 2–3 weeks of life. Kaposiform hemangioendothelioma ( KHE ) is a rare vascular tumor that typically presents as a violaceous to purpuric plaque at birth or early infancy. It may be associated with Kasabach‐Merritt phenomenon ( KMP ), a potentially life‐threatening consumptive coagulopathy.