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Congenital Kaposiform Hemangioendothelioma with Kasabach–Merritt Phenomenon Successfully Treated with Low‐Dose Radiation Therapy
Author(s) -
Malhotra Yogangi,
Yang Catherine S.,
McNamara Joseph,
Antaya Richard J.
Publication year - 2013
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.12090
Subject(s) - medicine , kasabach–merritt syndrome , radiation therapy , hemangioendothelioma , chemotherapy , consumptive coagulopathy , dermatology , surgery , radiology , hemangioma , coagulopathy
Kaposiform hemangioendothelioma (KHE) associated with Kasabach–Merritt phenomenon is a life‐threatening vasculopathy. The current mainstay treatment for KHEs is corticosteroids and chemotherapy, but these medications do not work for all patients and carry significant side effects. We report a neonate with a large congenital KHE who responded extremely well to low‐dose radiation therapy.