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Acquired Protein Energy Malnutrition in Glutaric Acidemia
Author(s) -
Ma Liqiao,
Savory Stephanie,
Agim Nnenna G.
Publication year - 2013
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.12067
Subject(s) - medicine , protein–energy malnutrition , malnutrition , pediatrics , intensive care medicine
We report a case of acquired protein energy malnutrition with associated zinc deficiency in an 18‐month‐old boy with type 1 glutaric acidemia. Physical examination findings included generalized nonpitting edema, widespread desquamative plaques, and sparse hair with a reddish tinge. Laboratory abnormalities included low levels of zinc, albumin, alkaline phosphatase, and iron. A review of skin manifestations of nutritional deficiencies, specifically kwashiorkor, is presented, as well as the relatively new entity called acrodermatitis dysmetabolica.