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Pediatric Primary Follicular Mucinosis: Further Evidence of its Relationship with Mycosis Fungoides
Author(s) -
SantosBriz Angel,
Cañueto Javier,
GarcíaDorado Jesus,
Teresa Alonso M.,
Balanzategui Ana,
GonzálezDíaz Marcos
Publication year - 2013
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/pde.12061
Subject(s) - mycosis fungoides , medicine , mucinosis , pathology , dermatology , follicular phase , lymphoma , mucin , lymphomatoid papulosis
Follicular mucinosis ( FM ) is an uncommon reaction pattern in which the accumulation of mucin in the follicular epithelium is the main pathologic finding. FM may be idiopathic (primary follicular mucinosis [ PFM ]), in association with mycosis fungoides or cutaneous T‐cell lymphoma, or in association with other neoplastic and inflammatory conditions. Herein we report a case of PFM with identical T‐cell clone rearrangement at anatomically distinct sites, supporting the idea that some authors have proposed, that FM may represent a low‐grade lymphoproliferative disease related to mycoses fungoides with favorable prognosis.