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Anesthesia management for ENT surgery in a child with X‐linked pyruvate kinase deficiency
Author(s) -
Hau Vickie,
BonillaVelez Juliana,
Low Daniel
Publication year - 2021
Publication title -
pediatric anesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.704
H-Index - 82
eISSN - 1460-9592
pISSN - 1155-5645
DOI - 10.1111/pan.14105
Subject(s) - medicine , ketamine , dexmedetomidine , anesthesia , anesthetic , pyruvate kinase , metabolism , endocrinology , glycolysis , sedation
Abstract Pyruvate dehydrogenase complex deficiency (PDCD) is a rare X‐linked disorder that affects glucose metabolism. There are several case reports describing the anesthetic management of patients with PDCD. This is the first case report to describe the anesthetic management of a PDCD patient requiring spontaneous ventilation using dexmedetomidine and ketamine.