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Perioperative considerations in infantile neuroaxonal dystrophy
Author(s) -
Sinskey Jina L.,
Holzman Robert S.
Publication year - 2017
Publication title -
pediatric anesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.704
H-Index - 82
eISSN - 1460-9592
pISSN - 1155-5645
DOI - 10.1111/pan.13081
Subject(s) - medicine , dystrophy , scoliosis , perioperative , muscular dystrophy , spinal fusion , surgery , pediatrics , anesthesia , pathology
Summary Infantile neuroaxonal dystrophy is a rare neurological disorder that is universally fatal with life expectancy under 10 years. A 10‐year‐old boy with infantile neuroaxonal dystrophy and severe neuromuscular scoliosis underwent posterior spinal fusion following halo traction. He was successfully extubated to bilevel positive airway pressure on postoperative day 3 and discharged home on postoperative day 11. Infantile neuroaxonal dystrophy presents several perioperative challenges including concerns for difficult intubation and respiratory dysfunction.