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Anesthetic considerations in S heldon– H all syndrome
Author(s) -
Anthony Anderson Thomas,
Kasser James R.,
Holzman Robert S.
Publication year - 2014
Publication title -
pediatric anesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.704
H-Index - 82
eISSN - 1460-9592
pISSN - 1155-5645
DOI - 10.1111/pan.12303
Subject(s) - arthrogryposis , medicine , muscle contracture , anesthetic , anesthesia , anatomy
Summary Arthrogryposis is characterized by multiple, nonprogressive joint contractures which may be caused by maternal disorders such as oligohydramnios as well as fetal akinesia resulting from primary disorders of muscle, connective tissue, or neurologic tissue. Its prevalence is about 1 : 3000. Distal arthrogryposis ( DA ) is a heterogenous group of genetic disorders with a characteristic flexion of the joints of the hands and feet divided into different types with additional features. Sheldon–Hall Syndrome ( SHS ), also known as distal arthrogryposis type 2A ( DA 2A), has some nonorthopedic features of specific importance to anesthetic care.