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Hemodynamic instability during prone spine surgery in a patient with merosin‐deficient congenital muscular dystrophy
Author(s) -
Jimenez Nathalia,
Song Kit,
Lynn Anne M.
Publication year - 2013
Publication title -
pediatric anesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.704
H-Index - 82
eISSN - 1460-9592
pISSN - 1155-5645
DOI - 10.1111/pan.12101
Subject(s) - medicine , muscular dystrophy , congenital muscular dystrophy , anesthesiology , anesthetic , weakness , hemodynamics , anesthesia , surgery
Summary Trans‐esophageal echocardiography ( TEE ) and/or central venous pressure ( CVP ) monitoring are important in the anesthetic management of spine fusion of pediatric patients with severe muscular weakness. This case highlights an unusual situation of apparent acute right ventricular mechanical obstruction after prone positioning and its prompt recognition with CVP monitoring. The anesthetic management of a patient with congenital muscular dystrophy, an uncommon neuromuscular disorder, is presented. Good communication and planning between the anesthesiology and surgical teams allowed completion of the procedure using a lateral approach.