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Cardiac intramural arteriovenous malformations presented as ventricular tachycardia and fibrillation storm
Author(s) -
Lim Kyunghee,
Park JongSung
Publication year - 2021
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/pace.14202
Subject(s) - medicine , cardiology , ventricular tachycardia , ventricular fibrillation , implantable cardioverter defibrillator , catheter ablation , hypertrophic cardiomyopathy , radiofrequency ablation , shock (circulatory) , sudden cardiac death , ablation
We report a case of cardiac intramural arteriovenous malformations (AVMs) misdiagnosed as hypertrophic cardiomyopathy and presented as life‐threatening ventricular arrhythmia storm that was successfully controlled by cardiac sympathetic denervation. A 46‐year‐old male patient with an implantable cardioverter‐defibrillator was admitted for recurrent ventricular tachycardia requiring repeated shock refractory to antiarrhythmic drugs. Although the patient was previously diagnosed with hypertrophic cardiomyopathy, multimodality imaging studies showed large left ventricular intramural AVMs, potentially representing arrhythmogenic substrates. Life‐threatening ventricular arrhythmia storm, which could not be controlled by radiofrequency catheter ablation and therapeutic hypothermia. However, cardiac sympathetic denervation surgery successfully controlled the ventricular arrhythmia storm.