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Primary intraosseous carcinoma, NOS in a 17‐year‐old male: case report and literature review
Author(s) -
Cox J.,
Shuren M.,
Chirila A.,
Darling M.R.
Publication year - 2020
Publication title -
oral surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.156
H-Index - 11
eISSN - 1752-248X
pISSN - 1752-2471
DOI - 10.1111/ors.12466
Subject(s) - medicine , malignancy , mandible (arthropod mouthpart) , odontogenic , surgery , pathology , biology , botany , genus
Primary intraosseous carcinoma (PIOC), NOS is a rare malignancy occurring in the jaw bones. It may arise de novo, or more commonly develop from pre‐existing lesions such as odontogenic cysts or tumours. In this manuscript, we describe a case of PIOC in the mandible of a 17‐year‐old male. Complicating factors were a history of familial hemophagocytic lymphohistiocytosis and Griscelli syndrome. Management included surgical removal and planned adjuvant chemoradiation. The relevant literature is reviewed with respect to PIOC in a paediatric population.