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Metastatic pleomorphic rhabdomyosarcoma to the mandible: report of a rare case and review of the literature
Author(s) -
Rizq M.,
Nawwar M.,
Ramadan O.
Publication year - 2020
Publication title -
oral surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.156
H-Index - 11
eISSN - 1752-248X
pISSN - 1752-2471
DOI - 10.1111/ors.12434
Subject(s) - medicine , rhabdomyosarcoma , metastasis , thigh , soft tissue , mandible (arthropod mouthpart) , undifferentiated pleomorphic sarcoma , soft tissue sarcoma , sarcoma , rare disease , surgery , pathology , disease , cancer , botany , biology , genus
Pleomorphic rhabdomyosarcoma is a rare and aggressive variant of rhabdomyosarcoma (RMS) that usually occurs only in adults aged 45 years or older. Jaw metastasis from a soft‐tissue sarcoma of the extremity is likewise very rare, with only a few previously reported cases. Here, we describe the case of a 47‐year‐old female patient with mandibular metastasis from a previously excised pleomorphic RMS of the right thigh but died 1 month after due to lung metastases. This is, to our knowledge, the first reported case of mandibular metastasis from pleomorphic rhabdomyosarcoma of the extremity. In cases such as these, patients may have widespread disease, and thus, surgery may only have a limited role in its management. Optimal treatment remains undefined.