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Extrapulmonary lymphangioleiomyomatosis mimicking lymphoma metastatic to uterus
Author(s) -
Vatansever Dogan,
Sozen Hamdullah,
Iyibozkurt A. Cem,
Comba Cihan,
Yavuz Ekrem,
Topuz Samet
Publication year - 2015
Publication title -
journal of obstetrics and gynaecology research
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.597
H-Index - 50
eISSN - 1447-0756
pISSN - 1341-8076
DOI - 10.1111/jog.12628
Subject(s) - lymphangioleiomyomatosis , medicine , pathology , lymphoma , uterus , tuberous sclerosis
Lymphangioleiomyomatosis is a very rare disease that primarily affects the lungs. The atypical smooth muscle cells in these tumors stain both with smooth muscle markers and melanocytic markers characteristically like their counterparts in other members of the PEC oma family. Extrapulmonary lymphangioleiomyomatosis, especially without pulmonary involvement, is extremely rare. The clinical importance of lymphangioleiomyomatosis lies in the fact that it may mimic other malignant diseases, such as lymphoma or sarcoma. Here, we report a case of extrapulmonary lymphangioleiomyomatosis without involvement of the lungs, in a patient pre‐diagnosed as having lymphoma metastasized to the uterus or uterine sarcoma.