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Congenital superior vena cava (SVC) stenosis and obstructed supracardiac total anomalous pulmonary venous connection (TAPVC)—A surgical perspective
Author(s) -
Mahajan Sachin,
Khanna Sudhansoo,
Rohit Manojkumar,
Chakraborty Nirupam S.,
Singhal Ankit
Publication year - 2020
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/jocs.14792
Subject(s) - medicine , total anomalous pulmonary venous connection , pulmonary vein stenosis , scimitar syndrome , superior vena cava , cardiology , stenosis , pulmonary valve stenosis , inferior vena cava , radiology , surgery , pulmonary vein , ablation
Congenital superior vena cava (SVC) stenosis is a very rare anomaly, especially in pediatric population. Coexistence with obstructed supracardiac total anomalous pulmonary venous connection (TAPVC) has never been reported. Clinical examination should prompt detailed and focused evaluation for this treatable etiology. Pericardial patch augmentation can cure SVC stenosis, and may allow for growth potential as well. We describe a case of congenital SVC stenosis in a case of obstructed supracardiac TAPVC in a 3‐month‐old infant, managed successfully.