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A surgical case of primary perivascular epithelioid cell tumor of the heart
Author(s) -
Daimon Masahiro,
Kanki Sachiko,
Ozawa Hideki,
Katsumata Takahiro
Publication year - 2020
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/jocs.14676
Subject(s) - perivascular epithelioid cell , medicine , immunostaining , epithelioid cell , pathology , cardiac tumors , immunohistochemistry , anatomy , radiology
Background We encountered an extremely rare case of perivascular epithelioid cell tumor (PEComa) of the heart. Case Report A 54‐year‐old woman was admitted to our hospital because a solid mass developing in the left atrioventricular groove by computed tomography scans of the chest. Histologic examination of the resected tumor revealed that the tumor had proliferating fusiform or spheroid cells with clear cytoplasm. Immunostaining showed positive results for α‐smooth muscle actin, a myogenic marker, and human melanin black‐45 (HMB‐45), leading to a diagnosis of PEComa. The patient was discharged uneventfully, and there was no recurrence for the last thirteen years postoperatively. Conclusions We experienced a surgical case of PEComa primarily occurring in the heart. Although no sign of a recurrence is observed to date, we consider it necessary to follow up the case carefully.