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Tricuspid atresia: Where are we now?
Author(s) -
Sumal Anoop S.,
Kyriacou Harry,
Mostafa Ahmed M. H. A. M.
Publication year - 2020
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/jocs.14673
Subject(s) - medicine , tricuspid atresia , etiology , presentation (obstetrics) , intensive care medicine , heart disease , intervention (counseling) , pathophysiology , pharmacotherapy , disease , pediatrics , general surgery , surgery , cardiology , psychiatry
Tricuspid atresia (TA) is a complex congenital heart disease that presents with cyanosis in the neonatal period. It is invariably fatal if left untreated and requires multiple stages of palliation. Early recognition and timely surgical intervention are therefore pivotal in the management of these infants. This literature review considers the pathophysiology, presentation, investigations, and classification of TA. Moreover, it discusses the evidence upon which the latest medical and surgical treatments are based, as well as numerous recent case reports. Further work is needed to elucidate the etiology of TA, clarify the role of pharmacotherapy, and optimize the surgical management that these patients receive.