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A rare childhood case of Behcet's disease and chronic thromboembolic pulmonary hypertension
Author(s) -
Wang Amy S.,
Rosenzweig Erika B.,
Takeda Koji
Publication year - 2020
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/jocs.14610
Subject(s) - medicine , behcet's disease , behcet disease , pulmonary hypertension , chronic thromboembolic pulmonary hypertension , pulmonary disease , rare disease , dermatology , thromboembolic disease , intensive care medicine , cardiology , disease , pediatrics , thrombosis
Background Pulmonary embolism and chronic thromboembolic pulmonary hypertension (CTEPH) are rare complications of Behcet's disease, especially in pediatric patients. Aims/Methods/Results/Conclusions This case report highlights a presentation of CTEPH in an adolescent with Behcet's disease. A multidisciplinary approach was required for managing this patient's CTEPH, which successfully reversed the patient's pulmonary hypertension.