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Gray platelet syndrome: Management of perioperative bleeding in redo cardiac surgery
Author(s) -
Carrascal Yolanda,
Laguna Gregorio,
Blanco Miriam,
Segura Bárbara,
MartínezAlmeida Iciar
Publication year - 2020
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/jocs.14354
Subject(s) - medicine , platelet , perioperative , cardiac surgery , surgery , cardiology
Gray platelet syndrome (GPS) is a rare (<1/1 000 000) and inherited platelet function disorder characterized by macrothrombocytopenia, α‐granule deficiency, and hemorrhages. Bleeding intensity does not correlate with platelet count nor with functional test results. We hereby describe the perioperative bleeding prevention and management of a patient with GPS requiring multiple redo cardiac surgeries.