Premium
Surgical repair of a truncus arteriosus with unilateral absence of the right proximal pulmonary artery
Author(s) -
Furuta Akihisa,
Nagashima Mitsugi,
Hiramatsu Takeshi,
Matsumura Goki,
Yamazaki Kenji
Publication year - 2016
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/jocs.12848
Subject(s) - medicine , truncus arteriosus , tetralogy of fallot , truncus , ventricular outflow tract , cardiology , pulmonary artery , right pulmonary artery , shunt (medical) , aortopulmonary window , surgery , left pulmonary artery , pulmonary atresia , heart disease
The unilateral absence of a proximal pulmonary artery (UAPPA) is rare and is most frequently accompanied by cardiovascular anomalies such as tetralogy of Fallot or septal defects. We report a patient with truncus arteriosus with UAPPA in which we performed a two‐stage surgical repair. During the first palliative operation, a right modified Blalock‐Taussig shunt was constructed to develop the hypoplastic right pulmonary artery. At 10 months, the patient underwent patch closure of a ventricular septal defect with integration of both pulmonary arteries, and reconstruction of the right ventricular outflow tract using a conduit. Four years postoperatively, he continues to do well.